Lysosomal storage disease search lysosomal storage diseases (lsds;   / ëœ l aéª s é™ ëˆ s oêš m é™l / ) are a group of approximately 50 rare inherited metabolic disorders that result from defects in lysosomal function. viagra viagra ingredients [1] lysosomal storage diseases result when the lysosome – a specific organelle in the body's cells – malfunctions. cheap generic viagra Lysosomal storage disorders are caused by lysosomal dysfunction usually as a consequence of deficiency of a single enzyme required for the metabolism of lipids, glycoproteins (sugar containing proteins) or so-called mucopolysaccharides. Individually, lsds occur with incidences of less than 1:100,000; however, as a group the incidence is about 1:5,000 - 1:10,000. buy viagra online cheapest Most of these disorders are autosomal recessively inherited such as niemann-pick disease, type c, however a few are x-linked recessively inherited, such as fabry disease and hunter syndrome (mps ii). buy viagra on line without prescription The lysosome is commonly referred to as the cell’s recycling center because it processes unwanted material into substances that the cell can utilize. buy viagra without prescription Lysosomes break down this unwanted matter via enzymes, highly specialized proteins essential for survival. Lysosomal disorders are triggered when a particular enzyme exists in too small an amount or is missing altogether. viagra women name When this happens, substances accumulate in the cell. In other words, when the lysosome doesn’t function normally, excess products destined for breakdown and recycling are stored in the cell. viagra online without prescription Like other genetic diseases, individuals inherit lysosomal storage diseases from their parents. viagra viagra ingredients Although each disorder results from different gene mutations that translate into a deficiency in enzyme activity, they all share a common biochemical characteristic – all lysosomal disorders originate from an abnormal accumulation of substances inside the lysosome. viagra daily and alcohol Lysosomal storage diseases affect mostly children and they often die at a young and unpredictable age, many within a few months or years of birth. genuine viagra no prescription Many other children die of this disease following years of suffering from various symptoms of their particular disorder. Source: wikipedia. viagra viagra ingredients News loading... Books loading... viagra cost Twitter top videos lyso. viagra sales Redirecting .... You will be redirected to a new page, if you are not redirected, please click here